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Icd-10 Chapter Xii: Diseases of the Skin and Subcutaneous Tissue Information

The International Statistical Classification of Diseases and Related Health Problems 10th Revision (ICD-10) is a coding of diseases and signs, symptoms, abnormal findings, complaints, social circumstances and external causes of injury or diseases, as classified by the World Health Organization (WHO).[1]. This page contains ICD-10 Chapter XII: Diseases of the skin and subcutaneous tissue.

Contents

L00–L99 – Diseases of the skin and subcutaneous tissue

(L00–L08) Infections of the skin and subcutaneous tissue

(L10–L14) Bullous disorders

(L20–L30) Dermatitis and eczema

(L40–L45) Papulosquamous disorders

(L50–L54) Urticaria and erythema

(L55–L59) Radiation-related disorders of the skin and subcutaneous tissue

(L60–L75) Disorders of skin appendages

(L80–L99) Other disorders of the skin and subcutaneous tissue

See also

References

  1. ^ WHO | International Classification of Diseases (ICD)
Pathology: Medical conditions and ICD code
(Disease / Disorder / Illness, Syndrome / Sequence, Symptom / Sign, Injury, etc.)
(A/B, 001–139) Infectious disease/Infection: Bacterial disease (G+, G-) · Virus disease · Parasitic disease (Protozoan infection, Helminthiasis, Ectoparasitic infestation) · Mycosis · Zoonosis
(C/D, 140–239 & 279–289)
Cancer (C00–D48, 140–239) Tumor
Myeloid hematologic (D50–D77, 280–289) Anemia · Coagulopathy
Lymphoid immune (D80–D89, 279) Immunodeficiency · Immunoproliferative disorder · Hypersensitivity
(E, 240–278) Endocrine disease · Nutrition disorder · Inborn error of metabolism
(F, 290–319) Mental disorder
(G, 320–359) Nervous system disease (CNS, PNS) · Neuromuscular disease
(H, 360–389) Eye disease · Ear disease
(I, 390–459) Cardiovascular disease (Heart disease, Vascular disease)
(J, 460–519) Respiratory disease (Obstructive lung disease, Restrictive lung disease, Pneumonia)
(K, 520–579) Stomatognathic disease (Tooth disease) · Digestive disease (Esophageal, Stomach, Enteropathy, Liver, Pancreatic)
(L, 680–709) Skin disease · skin appendages (Nail disease, Hair disease, Sweat gland disease)
(M, 710–739) Musculoskeletal disorders: Myopathy · Arthropathy · Osteochondropathy (Osteopathy, Chondropathy)
(N, 580–629) Urologic disease (Nephropathy, Urinary bladder disease) · Male genital disease · Breast disease · Female genital disease
(O, 630–679) Complications of pregnancy · Obstetric labor complication · Puerperal disorder
(P, 760–779) Fetal disease
(Q, 740–759) Congenital disorder (Congenital abnormality)
(R, 780–799) Syndromes · Medical signs (Eponymous)
(S/T, 800–999) Bone fracture · Joint dislocation · Sprain · Strain · Subluxation · Head injury · Chest trauma · Poisoning
Infectious skin disease: Bacterial skin disease (L00–L08, 680–686)
Gram +
Firmicutes Staphylococcus (Staphylococcal scalded skin syndrome, Impetigo, Toxic shock syndrome) · Streptococcus (Impetigo, Cutaneous group B streptococcal infection, Streptococcal intertrigo, Cutaneous Streptococcus iniae infection, Erysipelas/Chronic recurrent erysipelas, Scarlet fever) · Corynebacterium (Erythrasma) Listeriosis Clostridium (Gas gangrene, Dermatitis gangrenosa) Mycoplasma infection · Erysipeloid of Rosenbach
Actinobacteria Mycobacterium-related: Aquarium granuloma · Borderline lepromatous leprosy · Borderline leprosy · Borderline tuberculoid leprosy · Buruli ulcer · Erythema induratum · Histoid leprosy · Lepromatous leprosy · Leprosy · Lichen scrofulosorum · Lupus vulgaris · Miliary tuberculosis · Mycobacterium avium-intracellulare complex infection · Mycobacterium haemophilum infection · Mycobacterium kansasii infection · Papulonecrotic tuberculid · Primary inoculation tuberculosis · Rapid growing mycobacterium infection · Scrofuloderma · Tuberculosis cutis orificialis · Tuberculosis verrucosa cutis · Tuberculous cellulitis · Tuberculous gumma · Tuberculoid leprosy Cutaneous actinomycosis · Nocardiosis · Cutaneous diphtheria infection · Arcanobacterium haemolyticum infection · Group JK corynebacterium sepsis
Gram -
Proteobacteria α: Endemic typhus · Epidemic typhus · Scrub typhus · North Asian tick typhus · Queensland tick typhus · Flying squirrel typhus · Trench fever · Bacillary angiomatosis · African tick bite fever · American tick bite fever · Rickettsia aeschlimannii infection · Rickettsialpox · Rocky Mountain spotted fever · Human granulocytotropic anaplasmosis · Human monocytotropic ehrlichiosis · Flea-borne spotted fever · Japanese spotted fever · Mediterranean spotted fever · Flinders Island spotted fever · Verruga peruana · Brill–Zinsser disease · Brucellosis · Cat scratch disease · Oroya fever · Ehrlichiosis ewingii infection β: Gonococcemia/Gonorrhea/Primary gonococcal dermatitis · Melioidosis · Cutaneous Pasteurella hemolytica infection · Meningococcemia · Glanders · Chromobacteriosis infection γ: Pasteurellosis · Tularemia · Vibrio vulnificus infection · Rhinoscleroma · Haemophilus influenzae cellulitis · Pseudomonal pyoderma/Pseudomonas hot-foot syndrome/Hot tub folliculitis/Ecthyma gangrenosum/Green nail syndrome · Q fever · Salmonellosis · Shigellosis · Plague · Granuloma inguinale · Chancroid · Aeromonas infection ε: Helicobacter cellulitis
Other Syphilid · Syphilis · Chancre · Yaws · Pinta · Bejel · Chlamydial infection · Leptospirosis · Rat-bite fever · Lyme disease · Lymphogranuloma venereum ·
Unspecified pathogen Abscess (Periapical abscess) · Boil/furuncle (Hospital furunculosis) · Carbuncle · Cellulitis (Paronychia/Pyogenic paronychia, Perianal cellulitis) · Acute lymphadenitis · Pilonidal cyst · Pyoderma Folliculitis (Superficial pustular folliculitis, Sycosis vulgaris) · Pimple · Ecthyma · Pitted keratolysis · Trichomycosis axillaris · Necrotizing fascitis · Gangrene (Chronic undermining burrowing ulcers, Fournier gangrene) · Elephantiasis nostras · Blistering distal dactylitis · Botryomycosis · Malakoplakia · Gram-negative folliculitis · Gram-negative toe web infection · Pyomyositis · Blastomycosis-like pyoderma · Bullous impetigo · Chronic lymphangitis · Recurrent toxin-mediated perineal erythema · Tick-borne lymphadenopathy · Tropical ulcer ·

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Vesiculobullous disease (L10–L14
Acantholysis (epidermis)
Pemphigus
Other
Pemphigoid (dermis)
Other bullous
In diseases classified elsewhere

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Dermatitis and eczema (L20–L30, 690–693,698)
Atopic dermatitis Besnier's prurigo
Seborrheic dermatitis Pityriasis simplex capillitii · Cradle cap
Contact dermatitis (allergic, irritant) plants: Urushiol-induced contact dermatitis · African blackwood dermatitis · Tulip fingers other: Abietic acid dermatitis · Diaper rash · Airbag dermatitis · Baboon syndrome · Contact stomatitis · Protein contact dermatitis
Eczema Autoimmune estrogen dermatitis · Autoimmune progesterone dermatitis Breast eczema · Ear eczema · Eyelid dermatitis · Hand eczema (Chronic vesiculobullous hand eczema, Hyperkeratotic hand dermatitis) Autosensitization dermatitis/Id reaction (Candidid, Dermatophytid, Molluscum dermatitis) · Circumostomy eczema · Dyshidrosis · Juvenile plantar dermatosis · Nummular eczema · Nutritional deficiency eczema · Sulzberger–Garbe syndrome · Xerotic eczema
Pruritus/Itch/ Prurigo Lichen simplex chronicus/Prurigo nodularis by location: Pruritus ani · Pruritus scroti · Pruritus vulvae · Scalp pruritus Drug-induced pruritus (Hydroxyethyl starch-induced pruritus) · Senile pruritus · Aquagenic pruritus (Aquadynia) Adult blaschkitis · due to liver disease (Biliary pruritus · Cholestatic pruritus) · Prion pruritus · Prurigo pigmentosa · Prurigo simplex · Puncta pruritica · Uremic pruritus
Other/ungrouped substances taken internally: Bromoderma · Fixed drug reaction Nummular dermatitis · Pityriasis alba · Papuloerythroderma of Ofuji

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Papulosquamous disorders (L40–L45, 696–697)
Psoriasis
Pustular Generalized pustular psoriasis (Impetigo herpetiformis) · Acropustulosis/Pustulosis palmaris et plantaris (Pustular bacterid) · Annular pustular psoriasis · Localized pustular psoriasis
Other Guttate psoriasis · Psoriatic arthritis · Psoriatic erythroderma Drug-induced psoriasis · Inverse psoriasis · Napkin psoriasis · Seborrheic-like psoriasis
Parapsoriasis Pityriasis lichenoides (Pityriasis lichenoides et varioliformis acuta, Pityriasis lichenoides chronica) · Lymphomatoid papulosis · Small plaque parapsoriasis (Digitate dermatosis, Xanthoerythrodermia perstans) · Large plaque parapsoriasis (Retiform parapsoriasis)
Other pityriasis Pityriasis rosea · Pityriasis rubra pilaris · Pityriasis rotunda · Pityriasis amiantacea
Other lichenoid
Lichen planus

configuration: Annular lichen planus · Linear lichen planus

morphology of lesion: Hypertrophic lichen planus · Atrophic lichen planus · Bullous lichen planus · Ulcerative lichen planus · Lichen planus actinicus · Lichen planus pigmentosus

site of involvement: Mucosal lichen planus · Lichen planus of the nails · Peno-gingival syndrome · Vulvovaginal gingival syndrome

overlap: Lichen planus–lichen sclerosus overlap syndrome · Lichen planus–lupus erythematosus overlap syndrome

special forms: Hepatitis-associated lichen planus · Lichen planus pemphigoides
Other Lichen nitidus · Lichen striatus · Lichen ruber moniliformis · Gianotti–Crosti syndrome ungrouped lichenoid eruptions: Erythema dyschromicum perstans · Idiopathic eruptive macular pigmentation · Keratosis lichenoides chronica · Kraurosis vulvae · Lichen sclerosus · Lichenoid dermatitis · Lichenoid reaction of graft-versus-host disease

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Urticaria and erythema (L50–L54, 695, 708)
Urticaria (acute/chronic)
Allergic urticaria Urticarial allergic eruption
Physical urticaria Cold urticaria (Familial) · Primary cold contact urticaria · Secondary cold contact urticaria · Reflex cold urticaria Heat urticaria · Localized heat contact urticaria · Solar urticaria Dermatographic urticaria Vibratory angioedema · Pressure urticaria Cholinergic urticaria Aquagenic urticaria
Other urticaria Acquired C1 esterase inhibitor deficiency · Adrenergic urticaria · Exercise urticaria · Galvanic urticaria · Schnitzler syndrome · Urticaria-like follicular mucinosis
Angioedema Episodic angioedema with eosinophilia · Hereditary angioedema
Erythema
Erythema multiforme/ drug eruption Erythema multiforme minor · Erythema multiforme major (Stevens–Johnson syndrome, Toxic epidermal necrolysis) · panniculitis (Erythema nodosum) · Acute generalized exanthematous pustulosis
Figurate erythema Erythema annulare centrifugum · Erythema marginatum · Erythema migrans · Erythema gyratum repens
Other erythema Necrolytic migratory erythema · Erythema toxicum · Erythroderma · Palmar erythema · Generalized erythema

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Radiation-related disorders / Photodermatosis (L55–L59, 692.7)
Ultraviolet/ionizing

Sunburn · Phytophotodermatitis · Solar urticaria · Polymorphous light eruption (Benign summer light eruption, Juvenile spring eruption, Acne aestivalis) · Hydroa vacciniforme

Solar erythema
Nonionizing

Actinic rays: Actinic keratosis (Atrophic actinic keratosis · Hyperkeratotic actinic keratosis · Lichenoid actinic keratosis · Pigmented actinic keratosis) · Actinic cheilitis · Actinic granulomaActinic prurigoChronic actinic dermatitis

Infrared/heat: Erythema ab igne (Kangri ulcerKairo cancerKang cancerPeat fire cancer )

Cutis rhomboidalis nuchae · Poikiloderma of Civatte
Other/ungrouped

Radiation dermatitis (Acute radiodermatitis, Chronic radiodermatitis) · Favre–Racouchot syndrome

Photoaging • Photosensitivity with HIV infection • Phototoxic tar dermatitisPhytophotodermatitis

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Disorders of skin appendages (L60–L75, 703–706)
Nail thickness: Onychogryphosis · Onychauxis color: Beau's lines · Yellow nail syndrome · Leukonychia · Azure Lunula shape: Koilonychia · Nail clubbing behavior: Onychotillomania · Onychophagia other: Ingrown nail · Anonychia ungrouped: Paronychia (Acute paronychia, Chronic paronychia ) · Chevron nail · Congenital onychodysplasia of the index fingers · Green nails · Half and half nails · Hangnail · Hapalonychia · Hook nail · Lichen planus of the nails · Longitudinal erythronychia · Malalignment of the nail plate · Median nail dystrophy · Mees' lines · Melanonychia · Muehrcke's lines · Nail–patella syndrome · Onychoatrophy · Onychocryptosis · Onycholysis · Onychomadesis · Onychomatricoma · Onychomycosis · Onychophosis · Onychoptosis defluvium · Onychorrhexis · Onychoschizia · Platonychia · Pincer nails · Plummer's nail · Psoriatic nails · Pterygium inversum unguis · Pterygium unguis · Purpura of the nail bed · Racquet nail · Red lunulae · Shell nail syndrome · Splinter hemorrhage · Spotted lunulae · Staining of the nail plate · Stippled nails · Subungual hematoma · Terry's nails · Twenty-nail dystrophy
Hair
Hair loss/ Baldness noncicatricial alopecia: Alopecia/Alopecia areata (Alopecia totalis, Alopecia universalis, Ophiasis) Androgenic alopecia (male-pattern baldness) · Hypotrichosis · Telogen effluvium · Traction alopecia · Lichen planopilaris · Trichorrhexis nodosa · Alopecia neoplastica · Anagen effluvium · Alopecia mucinosa cicatricial alopecia: Pseudopelade of Brocq · Central centrifugal cicatricial alopecia · Pressure alopecia · Traumatic alopecia · Tumor alopecia · Hot comb alopecia · Perifolliculitis capitis abscedens et suffodiens · Graham-Little syndrome · Folliculitis decalvans ungrouped: Triangular alopecia · Frontal fibrosing alopecia · Marie Unna hereditary hypotrichosis
Hypertrichosis Hirsutism · Acquired generalized hypertrichosis · Generalized congenital hypertrichosis · Localized acquired hypertrichosis · Localized congenital hypertrichosis · Patterned acquired hypertrichosis · Prepubertal hypertrichosis · X-linked hypertrichosis
Acneiform eruption
Acne Acne vulgaris · Acne conglobata · Acne miliaris necrotica · Tropical acne · Infantile acne/Neonatal acne · Excoriated acne · Acne fulminans · Acne medicamentosa (e.g., steroid acne) · Halogen acne (Iododerma, Bromoderma, Chloracne) · Oil acne · Tar acne · Acne cosmetica · Occupational acne · Acne aestivalis · Acne keloidalis nuchae · Acne mechanica · Acne with facial edema · Pomade acne · Acne necrotica · Blackhead · Lupus miliaris disseminatus faciei
Rosacea Perioral dermatitis (Granulomatous perioral dermatitis) · Phymatous rosacea (Rhinophyma, Blepharophyma, Gnathophyma, Metophyma, Otophyma) · Papulopustular rosacea · Lupoid rosacea · Erythrotelangiectatic rosacea · Glandular rosacea · Gram-negative rosacea · Steroid rosacea · Ocular rosacea · Persistent edema of rosacea · Rosacea conglobata · variants (Periorificial dermatitis, Pyoderma faciale)
Ungrouped Granulomatous facial dermatitis · Idiopathic facial aseptic granuloma · Periorbital dermatitis · SAPHO syndrome
Follicular cysts Epidermoid cyst · Trichilemmal cyst · Sebaceous cyst · Steatocystoma multiplex · Milia
Inflammation Folliculitis (Folliculitis nares perforans, Tufted folliculitis) · Pseudofolliculitis barbae Hidradenitis (Hidradenitis suppurativa, Recurrent palmoplantar hidradenitis, Neutrophilic eccrine hidradenitis)
Ungrouped Acrokeratosis paraneoplastica of Bazex · Acroosteolysis · Bubble hair deformity · Disseminate and recurrent infundibulofolliculitis · Erosive pustular dermatitis of the scalp · Erythromelanosis follicularis faciei et colli · Hair casts · Hair follicle nevus · Intermittent hair–follicle dystrophy · Keratosis pilaris atropicans · Kinking hair · Koenen's tumor · Lichen planopilaris · Lichen spinulosus · Loose anagen syndrome · Menkes kinky hair syndrome · Monilethrix · Parakeratosis pustulosa · Pili (Pili annulati · Pili bifurcati · Pili multigemini · Pili pseudoannulati · Pili torti) · Pityriasis amiantacea · Plica neuropathica · Poliosis · Rubinstein–Taybi syndrome · Setleis syndrome · Traumatic anserine folliculosis · Trichomegaly · Trichomycosis axillaris · Trichorrhexis (Trichorrhexis invaginata · Trichorrhexis nodosa) · Trichostasis spinulosa · Uncombable hair syndrome · Wooly hair · Wooly hair nevus
Sweat glands
Eccrine Miliaria (Colloid miliumMiliaria crystallineMiliaria profundaMiliaria pustulosaMiliaria rubraOcclusion miliariaPostmiliarial hypohidrosis), Granulosis rubra nasi, Ross’ syndrome, Anhidrosis, Hyperhidrosis (Generalized, Gustatory, Palmoplantar)
Apocrine Body odor, Chromhidrosis, Fox–Fordyce disease
Sebaceous Sebaceous hyperplasia

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Pigmentation disorders/Dyschromia (L80–L81, 709.0)
Hypo-/ leucism
Loss of melanocytes

vitiligo: Quadrichrome vitiligo · Vitiligo ponctué · syndromic (Alezzandrini syndrome · Vogt–Koyanagi–Harada syndrome)

melanocyte development: Piebaldism · Waardenburg syndrome · Tietz syndrome
Loss of melanin/ amelanism

albinism: Oculocutaneous albinism · Ocular albinism

melanosome transfer: Hermansky–Pudlak syndrome · Chédiak–Higashi syndrome · Griscelli syndrome (Elejalde syndrome · Griscelli syndrome type 2 · Griscelli syndrome type 3)

other: Cross syndrome · ABCD syndrome · Albinism–deafness syndrome · Idiopathic guttate hypomelanosis · Phylloid hypomelanosis · Progressive macular hypomelanosis
Leukoderma w/o hypomelanosis Vasospastic macule · Woronoff's ring · Nevus anemicus
Ungrouped ungrouped: Nevus depigmentosus · Postinflammatory hypopigmentation · Pityriasis alba · Vagabond's leukomelanoderma · Yemenite deaf-blind hypopigmentation syndrome · Wende–Bauckus syndrome
Hyper-
Melanin/ Melanosis/ Melanism
Reticulated Dermatopathia pigmentosa reticularis · Pigmentatio reticularis faciei et colli · Reticulate acropigmentation of Kitamura · Reticular pigmented anomaly of the flexures · Naegeli–Franceschetti–Jadassohn syndrome · Dyskeratosis congenita · X-linked reticulate pigmentary disorder · Galli–Galli disease · Revesz syndrome
Diffuse/ circumscribed

Lentigo/Lentiginosis: Lentigo simplex · Liver spot · Centrofacial lentiginosis · Generalized lentiginosis · Inherited patterned lentiginosis in black persons · Ink spot lentigo · Lentigo maligna · Mucosal lentigines · Partial unilateral lentiginosis · PUVA lentigines

Melasma · Erythema dyschromicum perstans · Lichen planus pigmentosus · Café au lait spot · Poikiloderma (Poikiloderma of Civatte · Poikiloderma vasculare atrophicans) · Riehl melanosis
Linear Incontinentia pigmenti · Scratch dermatitis · Shiitake mushroom dermatitis
Other/ungrouped Acanthosis nigricans (Acral acanthotic anomaly) · Freckle · Familial progressive hyperpigmentation · Pallister–Killian syndrome · Periorbital hyperpigmentation · Photoleukomelanodermatitis of Kobori · Postinflammatory hyperpigmentation · Transient neonatal pustular melanosis
Other pigments iron: Hemochromatosis · Iron metallic discoloration · Pigmented purpuric dermatosis (Schamberg disease, Majocchi's disease, Gougerot–Blum syndrome, Doucas and Kapetanakis pigmented purpura/Eczematid-like purpura of Doucas and Kapetanakis, Lichen aureus, Angioma serpiginosum) · Hemosiderin hyperpigmentation other metals: Argyria · Chrysiasis · Arsenic poisoning · Lead poisoning · Titanium metallic discoloration other: Carotenosis · Tattoo · Tar melanosis
Dyschromatoses Dyschromatosis symmetrica hereditaria · Dyschromatosis universalis hereditaria

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Cutaneous keratosis, ulcer, atrophy, and necrobiosis (L82–L94, 700–701.5)
Epidermal thickening

keratoderma: Keratoderma climactericumParaneoplastic keratoderma (Acrokeratosis paraneoplastica of Bazex ) • Aquagenic keratoderma · Drug-induced keratoderma · Paraneoplastic keratodermapsoriasis (Keratoderma blennorrhagica)

keratosis: Seborrheic keratosis (Clonal seborrheic keratosis · Common seborrheic keratosis · Irritated seborrheic keratosis · Seborrheic keratosis with squamous atypia · Reticulated seborrheic keratosis · Dermatosis papulosa nigra) • Keratosis punctata of the palmar creases

other hyperkeratosis: Acanthosis nigricans (Confluent and reticulated papillomatosis) · CallusIchthyosis acquisita · Arsenical keratosis · Chronic scar keratosis · Hyperkeratosis lenticularis perstans · Hydrocarbon keratosis · Hyperkeratosis of the nipple and areola · Inverted follicular keratosis · Lichenoid keratosis · Multiple minute digitate hyperkeratosis · PUVA keratosis · Reactional keratosis · Stucco keratosis · Thermal keratosis · Viral keratosis · Warty dyskeratoma · Waxy keratosis of childhood

other hypertrophy: Keloid · Hypertrophic scarCutis verticis gyrata ·
Necrobiosis/granuloma
Necrobiotic/palisading Granuloma annulare (Perforating, Generalized, Subcutaneous, Granuloma annulare in HIV disease, Localized granuloma annulare, Patch-type granuloma annulare) · Necrobiosis lipoidica · Annular elastolytic giant cell granuloma · Granuloma multiforme · Necrobiotic xanthogranuloma · Palisaded neutrophilic and granulomatous dermatitis · Rheumatoid nodulosis · Interstitial granulomatous dermatitis/Interstitial granulomatous drug reaction
Foreign body granuloma Beryllium granulomaMercury granulomaSilica granulomaSilicone granulomaZirconium granulomaSoot tattooTattooCarbon stain
Other/ungrouped eosinophilic dermatosis (Granuloma faciale)
Dermis/ localized CTD
Cutaneous lupus erythematosus chronic: Discoid · Panniculitis subacute: Neonatal ungrouped: Chilblain · Lupus erythematosus–lichen planus overlap syndrome · Tumid · Verrucous · Rowell's syndrome
Scleroderma/ Morphea Localized scleroderma (Localized morphea, Morphea–lichen sclerosus et atrophicus overlap, Generalized morphea, Atrophoderma of Pasini and Pierini, Pansclerotic morphea, Morphea profunda, Linear scleroderma)
Atrophic/ atrophoderma Lichen sclerosus · Anetoderma (Schweninger–Buzzi anetoderma, Jadassohn–Pellizzari anetoderma) · Atrophoderma of Pasini and Pierini · Acrodermatitis chronica atrophicans · Semicircular lipoatrophy · Follicular atrophoderma · Linear atrophoderma of Moulin
Perforating Kyrle disease · Reactive perforating collagenosis · Elastosis perforans serpiginosa · Perforating folliculitis · Acquired perforating dermatosis
Skin ulcer Pyoderma gangrenosum
Other Calcinosis cutis · Sclerodactyly · Poikiloderma vasculare atrophicans · Ainhum/Pseudo-ainhum

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Cutaneous vasculitis and other vascular-related cutaneous conditions (L95, 709.1)
Cutaneous vasculitis Erythema elevatum diutinum · Capillaritis · Urticarial vasculitis · Nodular vasculitis
Microvascular occlusion

Calciphylaxis · Cryoglobulinemic purpura/Cryoglobulinemic vasculitis

vascular coagulopathy: Livedoid vasculitis (Livedoid dermatitis, Perinatal gangrene of the buttock) · Malignant atrophic papulosis · Sneddon's syndrome
Purpura

Nonthrombocytopenic purpura: Cryofibrinogenemic purpura · Drug-induced purpura · Food-induced purpura · Henoch–Schönlein purpura · Obstructive purpura · Orthostatic purpura · Purpura fulminans · Purpura secondary to clotting disorders · Purpuric agave dermatitis · Pigmentary purpuric eruptions · Solar purpura · Traumatic purpura · Waldenström hyperglobulinemic purpura · Painful bruising syndrome

ungrouped: Paroxysmal hand hematoma · Postcardiotomy syndrome · Deep venous thrombosis · Superficial thrombophlebitis · Mondor's disease · Blueberry muffin baby · Fibrinolysis syndrome
Systemic vasculitis see
Vascular malformations

Arteriovenous malformation (Bonnet–Dechaume–Blanc syndrome, Cobb syndrome, Parkes Weber syndrome) · Sinusoidal hemangioma · lymphatic malformation (Hennekam syndrome, Aagenaes syndrome)

telangiectasia: Generalized essential telangiectasia · Hereditary hemorrhagic telangiectasia · Unilateral nevoid telangiectasia
Ulcer Venous insufficiency ulceration · Arterial insufficiency ulcer · Hematopoietic ulcer · Neuropathic ulcer · Acroangiodermatitis
Lymphedema see
Ungrouped vascular-related cutaneous conditions Raynaud phenomenon · Raynaud's disease · Thromboangiitis obliterans · Erythromelalgia · Septic thrombophlebitis · Arteriosclerosis obliterans · Bier spots/Marshall–White syndrome · Cholesterol embolus · Reactive angioendotheliomatosis · Trousseau's syndrome

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Factitial dermatitis (F45.8+L98.1, 306.3+698.4) and psychiatric and organic nervous system disease / neurodermatitis
F Body dysmorphic disorder · Bromidrosiphobia · Delusional parasitosis · Dermatothlasia · Factitious dermatitis · Trichotillomania
G Complex regional pain syndrome · Congenital insensitivity to pain with anhidrosis · Meralgia paraesthetica · Riley–Day syndrome · Sciatic nerve injury · Syringomyelia · Trigeminal neuralgia
K Glossodynia
L Malum perforans pedis · Neurotic excoriations · Factitial lymphedema
Ungrouped Atypical chronic pain syndrome · Brachioradial pruritus · Notalgia paresthetica · Postencephalitic trophic ulcer · Psychogenic pruritus · Scalp dysesthesia · Scrotodynia/Vulvodynia · Traumatic neuroma · Trigeminal trophic lesion

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Neutrophilic and eosinophilic dermatoses (L98.2-3)
Eosinophilic dermatosis
With vasculitis Eosinophilic vasculitisChurg–Strauss syndrome
Without vasculitis Arthropod assaultEosinophilic cellulitisHypereosinophilic syndromePapuloerythroderma of OfujiGranuloma facialeEosinophilic folliculitis
Ungrouped Angiolymphoid hyperplasia with eosinophilia/Kimura's diseaseAnnular erythema of infancyEosinophilic fasciitisEosinophilic granuloma • Eosinophilic ulcer of the oral mucosa • Erythema toxicum neonatorumIncontinentia pigmentiItchy red bump diseaseJuvenile xanthogranulomaPachydermatous eosinophilic dermatitisPapular eruption of blacks • Pruritic papular eruption of HIV disease
Reactive neutrophilic dermatoses
Epidermis Keratoderma blennorrhagicaSubcorneal pustular dermatosis
Dermis

without vasculitis: Sweet's syndromePyoderma gangrenosumBowel-associated dermatosis–arthritis syndrome

with vasculitis: Neutrophilic dermatosis of the dorsal hands
Ungrouped Acute erythema nodosumMarshall syndromeNeutrophilic eccrine hidradenitisPyogenic arthritis–pyoderma gangrenosum–acne syndromeRheumatoid neutrophilic dermatitisSuperficial granulomatous pyodermaSweet's syndrome-like dermatosisVesicopustular dermatosis

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Mucinosis/Lichen myxedematosus (L98.5, 701.8)
Localized lichen myxedematosus Discrete papular lichen myxedematosus · Acral persistent papular mucinosis · Self-healing papular mucinosis/Self-healing juvenile cutaneous mucinosis · Papular mucinosis of infancy · Atypical lichen myxedematosus · Atypical tuberous myxedema · Nodular lichen myxedematosus
Other primary mucinoses

Cutaneous focal mucinosis · Cutaneous lupus mucinosis · Eccrine mucinosis · Alopecia mucinosa · Perifollicular mucinosis · Stiff skin syndrome

Generalized lichen myxedematosus
Secondary mucinoses Basal cell carcinoma · Granuloma annulare

: INT, SF, LCT

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