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Necrobiosis Lipoidica Information

Necrobiosis lipoidica is a necrotizing skin condition that usually occurs in patients with diabetes but can also be associated with Rheumatoid Arthritis.[1]:539 In such cases it may be called necrobiosis lipoidica diabeticorum (NLD). NLD occurs in approximately 0.3% of the diabetic population, with the majority of sufferers being women (approximately 90%).

Necrobiosis lipoidica is closely related to granuloma annulare.

Contents

Clinical appearance

NL/NLD most frequently appears on the patient's shins, often on both legs. The lesions are often tender and may become yellowish in the centre and ulcerate when injured. The first symptom of NL/NLD is often a "bruised" appearance (erythematous) that is not necessarily associated with a known injury. The extent to which NL/NLD is inherited is not known.

See also

References

  1. ^ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.

External links

Diseases of the skin and appendages by morphology
Growths
Epidermal wart · callus · seborrheic keratosis · acrochordon · molluscum contagiosum · actinic keratosis · squamous cell carcinoma · basal cell carcinoma · merkel cell carcinoma · nevus sebaceous · trichoepithelioma
Pigmented Freckles · lentigo · melasma · nevus · melanoma
Dermal and subcutaneous epidermal inclusion cyst · hemangioma · dermatofibroma · keloid · lipoma · neurofibroma · xanthoma · Kaposi's sarcoma · infantile digital fibromatosis · granular cell tumor · leiomyoma · lymphangioma circumscriptum · myxoid cyst
Rashes
With epidermal involvement
Eczematous contact dermatitis · atopic dermatitis · seborrheic dermatitis · stasis dermatitis · lichen simplex chronicus · Darier's disease · glucagonoma syndrome · langerhans cell histiocytosis · lichen sclerosus · pemphigus foliaceus · Wiskott-Aldrich syndrome · Zinc deficiency
Scaling psoriasis · tinea (corporis · cruris · pedis · manuum · faciei) · pityriasis rosea · secondary syphillis · mycosis fungoides · systemic lupus erythematosus · pityriasis rubra pilaris · parapsoriasis · ichthyosis
Blistering herpes simplex · herpes zoster · varicella · bullous impetigo · acute contact dermatitis · pemphigus vulgaris · bullous pemphigoid · dermatitis herpetiformis · porphyria cutanea tarda · epidermolysis bullosa simplex
Papular scabies · insect bite reactions · lichen planus · miliaria · keratosis pilaris · lichen spinulosus · transient acantholytic dermatosis · lichen nitidus · pityriasis lichenoides et varioliformis acuta
Pustular acne vulgaris · acne rosacea · folliculitis · impetigo · candidiasis · gonococcemia · dermatophyte · coccidioidomycosis · subcorneal pustular dermatosis
Hypopigmented tinea versicolor · vitiligo · pityriasis alba · postinflammatory hyperpigmentation · tuberous sclerosis · idiopathic guttate hypomelanosis · leprosy · hypopigmented mycosis fungoides
Without epidermal involvement
Red
Blanchable Erythema
Generalized drug eruptions · viral exanthems · toxic erythema · systemic lupus erythematosus
Localized cellulitis · abscess · boil · erythema nodosum · carcinoid syndrome · fixed drug eruption
Specialized urticaria · erythema (multiforme · migrans · gyratum repens · annulare centrifugum · ab igne)
Nonblanchable Purpura
Macular thrombocytopenic purpura · actinic purpura
Papular disseminated intravascular coagulation · vasculitis
Indurated scleroderma/morphea · granuloma annulare · lichen sclerosis et atrophicus · necrobiosis lipoidica
Miscellaneous disorders
Ulcers
Hair telogen effluvium · androgenic alopecia · trichotillomania · alopecia areata · systemic lupus erythematosus · tinea capitis · loose anagen syndrome · lichen planopilaris · folliculitis decalvans · acne keloidalis nuchae
Nail onychomycosis · psoriasis · paronychia · ingrown nail
Mucous membrane aphthous stomatitis · oral candidiasis · lichen planus · leukoplakia · pemphigus vulgaris · mucous membrane pemphigoid · cicatricial pemphigoid · herpesvirus · coxsackievirus · syphilis · systemic histoplasmosis · squamous cell carcinoma
Cutaneous keratosis, ulcer, atrophy, and necrobiosis (L82-L94, 700-701.5)
Epidermal thickening/ keratoderma/ keratosis/ hyperkeratosis
PPK
Inherited

diffuse: Diffuse epidermolytic palmoplantar keratodermaDiffuse nonepidermolytic palmoplantar keratodermaPalmoplantar keratoderma of SybertMal de Meleda • syndromic (connexin (Bart–Pumphrey syndromeClouston's hidrotic ectodermal dysplasiaVohwinkel syndrome) • Corneodermatoosseous syndromeplakoglobin (Naxos syndrome) • Scleroatrophic syndrome of HuriezOlmsted syndromeCathepsin C (Papillon–Lefèvre syndromeHaim–Munk syndrome) • Camisa disease

focal: Focal palmoplantar keratoderma with oral mucosal hyperkeratosis • Focal palmoplantar and gingival keratosisHowel–Evans syndromePachyonychia congenita (Pachyonychia congenita type IPachyonychia congenita type II) • Striate palmoplantar keratodermaTyrosinemia type II)

punctate: Acrokeratoelastoidosis of CostaFocal acral hyperkeratosisKeratosis punctata palmaris et plantarisKeratosis punctata of the palmar creasesSchöpf–Schulz–Passarge syndromePorokeratosis plantaris discretaSpiny keratoderma

ungrouped: Palmoplantar keratoderma and spastic paraplegiadesmoplakin (Carvajal syndrome) • connexin (Erythrokeratodermia variabilisHID/KID)
Acquired Keratoderma climactericumParaneoplastic keratodermaAcrokeratosis paraneoplastica of BazexAquagenic keratoderma
Other Acanthosis nigricans · Keloid · Seborrheic keratosis · CallusKeratoderma blennorrhagicaIchthyosis acquisita
Skin ulcer Pyoderma gangrenosum
Atrophic/atrophoderma Lichen sclerosus · Anetoderma (Schweninger–Buzzi anetoderma, Jadassohn–Pellizzari anetoderma) · Atrophoderma of Pasini and Pierini · Acrodermatitis chronica atrophicans · Semicircular lipoatrophy · Follicular atrophoderma · Linear atrophoderma of Moulin
Necrobiosis/granuloma

necrobiotic/palisading: Granuloma annulare (Perforating, Generalized, Subcutaneous, Granuloma annulare in HIV disease, Localized granuloma annulare, Patch-type granuloma annulare) · Necrobiosis lipoidica · Annular elastolytic giant cell granuloma · Granuloma multiforme · Necrobiotic xanthogranuloma · Palisaded neutrophilic and granulomatous dermatitis · Rheumatoid nodulosis

foreign body granuloma: Silica granuloma

miscellaneous/other: Granuloma faciale · Sclerosing lipogranuloma · Pyogenic granuloma · Interstitial granulomatous drug reaction · Interstitial granulomatous dermatitis
Localized CTD
Cutaneous lupus erythematosus

chronic: Discoid · Panniculitis

subacute: Neonatal

ungrouped: Chilblain · Lupus erythematosus–lichen planus overlap syndrome · Tumid · Verrucous · Rowell's syndrome
Scleroderma/ Morphea Localized scleroderma (Localized morphea, Morphea–lichen sclerosus et atrophicus overlap, Generalized morphea, Atrophoderma of Pasini and Pierini, Pansclerotic morphea, Morphea profunda, Linear scleroderma)
Other Calcinosis cutis · Sclerodactyly · Poikiloderma vasculare atrophicans · Ainhum/Pseudo-ainhum
Transepidermal elimination Kyrle disease · Reactive perforating collagenosis · Elastosis perforans serpiginosa

: INT, SF, LCT

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Categories: Skin conditions resulting from errors in metabolism | Diabetes |

 

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